Pendahuluan Tetralogy of Fallot

Oleh :

dr.Gold SP Tampubolon

Tetralogy of Fallot yang pertama kali dideskripsikan oleh Etienne-Louis Fallot merupakan salah satu kelainan jantung kongenital dengan defek utama pada septum infundibular dimana terdapat empat komponen defek, yaitu:

Stenosis pulmonal

Ventricular septal defect (VSD)

Overriding aorta

Hipertrofi ventrikel kanan

Gejala Tetralogy of Fallot muncul pada masa awal kehidupan, biasanya ditandai dengan sianosis dan terdengar murmur pada pemeriksaan fisik. Ekhokardiografi dapat digunakan sebagai pemeriksaan penunjang untuk mengetahui letak defek jantung.

Tetralogy of Fallot merupakan kelainan jantung sianotik kongenital yang paling sering terjadi dengan perkiraan kejadian 1 per 3500 kelahiran hidup. Tata laksana bedah merupakan tatalaksana definitif bagi pasien Tetralogy of Fallot, yang dapat bersifat korektif maupun paliatif. Pasien Tetralogy of Fallot yang telah dilakukan operasi korektif sebanyak 94% dapat mencapai umur 25 tahun.

Tetralogy of Fallot. Sumber: anonim, Openi, 2013.

Referensi

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15. Geva T. Indications for Pulmonary Valve Replacement in Repaired Tetralogy of Fallot. Circulation. 2013 Oct 21;128(17):1855 LP-1857. Available from: http://circ.ahajournals.org/content/128/17/1855.abstract

16. Cuypers JAAE, Menting ME, Konings EEM, Opić P, Utens EMWJ, Helbing WA, et al. The Unnatural History of Tetralogy of Fallot: Prospective Follow-Up of 40 Years After Surgical Correction. Circulation. 2014 Oct 23; Available from: http://circ.ahajournals.org/content/early/2014/10/23/CIRCULATIONAHA.114.009454.abstract

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18. Kamiya CA, Iwamiya T, Neki R, Katsuragi S, Kawasaki K, Miyoshi T, et al. Outcome of Pregnancy and Effects on the Right Heart in Women With Repaired Tetralogy of Fallot. Circ J. 2012;76(4):957–63. Available from: http://dx.doi.org/10.1253/circj.CJ-11-1239

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Pendahuluan Tetralogy of Fallot

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